akusherstvoObstetrics, Gynecology and ReproductionАкушерство, Гинекология и Репродукция2313-73472500-3194IRBIS LLC10.17749/2313-7347/ob.gyn.rep.2023.419akusherstvo-1819Research ArticleCLINICAL CASEКЛИНИЧЕСКИЙ СЛУЧАЙMayer–Rokitansky–Küster–Hauser syndromeСиндром Майера–Рокитанского–Кюстера–Хаузераhttps://orcid.org/0000-0001-9357-633XАдамянР. Т.AdamyanR. T.

Адамян Рубен Татевосович – д.м.н., профессор отделения пластической, реконструктивной и челюстно-лицевой хирургии; профессор кафедры онкологии, радиотерапии и реконструктивной хирургии

119991 Москва, Ленинские горы, д. 1

109004 Москва, ул. Земляной Вал, д. 62

Ruben T. Adamyan – MD, Dr Sci Med, Professor, Department of Plastic, Reconstructive and Maxillofacial Surgery; Professor, Department of Oncology, Radiotherapy and Plastic Surgery

1 Leninskie Gory, Moscow 119991

62 Str. Zemlyanoi Val, Moscow 109004

https://orcid.org/0009-0007-2140-6797БлбулянА. К.BlbulyanA. K.

Блбулян Армен Кимович – д.м.н., зам. директора по научной работе

0078 Ереван, ул. Маркаряна, д. 6/2

Armen K. Blbulyan – MD, Dr Sci Med, Deputy Director for Science

6/2 Markaryan Str., Yerevan 0078

belbulyan@mail.ruhttps://orcid.org/0009-0007-0964-4231АбрамянР. А.AbrahamyanR. A.

Абрамян Размик Аршалуйсович – д.м.н., профессор, академик НАН Республики Армения, директор

0078 Ереван, ул. Маркаряна, д. 6/2

Razmik A. Abrahamyan – MD, Dr Sci Med, Professor, Director

6/2 Markaryan Str., Yerevan 0078

https://orcid.org/0009-0001-7013-3082АбрамянЛ. Р.AbrahamyanL. R.

Абрамян Лусине Размиковна – д.м.н., профессор, зав. кафедрой акушерства и гинекологии № 2

Ереван 0025, ул. Корюна, д. 2

Lusine R. Abrahamyan – MD, Dr Sci Med, Professor, Head of the Department of Obstetrics and Gynecology No. 2

 2 Koryun Str., Yerevan 0025

https://orcid.org/0009-0001-8727-8798АбрамянГ. Р.AbrahamyanG. R.

Абрамян Гоар Размиковна – д.м.н., доцент кафедры акушерства и гинекологии № 2

Ереван 0025, ул. Корюна, д. 2

 

Gohar R. Abrahamyan – MD, Dr Sci Med, Associate Professor, Department of Obstetrics and Gynecology No. 2

 2 Koryun Str., Yerevan 0025

https://orcid.org/0009-0002-3430-884XГардянГ. К.GhardyanG. K.

Гардян Гегам Карапетович – ассистент кафедры патологической анатомии и клинической морфологии, клинический ординатор кафедры акушерства и гинекологии № 2

Ереван 0025, ул. Корюна, д. 2

Gegham K. Ghardyan – MD, Assistant, Department of Pathological Anatomy and Clinical Morphology; Clinical Resident, Department of Obstetrics and Gynecology No. 2

 2 Koryun Str., Yerevan 0025

https://orcid.org/0009-0006-8197-4342БлбулянД. А.BlbulyanD. A.

Блбулян Давид Арменович – клинический ординатор кафедрыакушерства,гинекологии и перинатологии

109004 Москва, ул. Земляной Вал, д. 62

David A. Blbulyan – MD, Clinical Resident, Department of Obstetrics, Gynecology and Perinatal Medicine

62 Str. Zemlyanoi Val, Moscow 109004

Медицинский научно-образовательный центр ФГБОУ ВО «Московский государственный университет имени М.В. Ломоносова»; ФГАОУ ВО «Первый Московский государственный медицинский университет имени И.М. Сеченова» Министерства здравоохранения Российской Федерации (Сеченовский Университет)РоссияMedical Research and Education Center, Lomonosov Moscow State University; Sechenov UniversityRussian FederationРеспубликанский институт репродуктивного здоровья, перинатологии, акушерства и гинекологииАрменияRepublican Institute of Reproductive Health, Perinatology, Obstetrics and GynecologyArmeniaЕреванский государственный медицинский университет имени Мхитара ГерациАрменияHeratsi Yerevan State Medical UniversityArmeniaФГАОУ ВО «Первый Московский государственный медицинский университет имени И.М. Сеченова» Министерства здравоохранения Российской Федерации (Сеченовский Университет)РоссияSechenov UniversityRussian Federation202311112023175654662Copyright © Adamyan R.T., Blbulyan A.K., Abrahamyan R.A., Abrahamyan L.R., Abrahamyan G.R., Ghardyan G.K., Blbulyan D.A., 20232023Адамян Р.Т., Блбулян А.К., Абрамян Р.А., Абрамян Л.Р., Абрамян Г.Р., Гардян Г.К., Блбулян Д.А.Adamyan R.T., Blbulyan A.K., Abrahamyan R.A., Abrahamyan L.R., Abrahamyan G.R., Ghardyan G.K., Blbulyan D.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.gynecology.su/jour/article/view/1819

The Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome is an instructive story not only from a historical but also a gnoseological perspective. The mechanisms of embryogenesis as well as multiple aspects for correction of this syndrome remain enigmatic and unsolved. Here, we attempted to organize and detail striking issues related to MRKH syndrome.

История синдрома Майера–Рокитанского–Кюстера–Хаузера (СМРКХ) поучительна не только с исторической точки зрения, но и с гносеологической. Остаются загадкой не только механизмы эмбриогенеза, но не решены многие хирургические аспекты коррекции данного синдрома. Сделана попытка упорядочить и детализировать наиболее интересные аспекты синдрома.

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The authors declare that there are no conflicts of interest present.